What does Dandy Walker syndrome affect?
Dandy-Walker malformation affects brain development, primarily development of the cerebellum, which is the part of the brain that coordinates movement. In individuals with this condition, various parts of the cerebellum develop abnormally, resulting in malformations that can be observed with medical imaging.
When is Dandy-Walker diagnosed?
Symptoms of Dandy-Walker malformation usually appear by age 1. These symptoms may include: Developmental delays in motor and language skills such as sitting up, walking and talking. Poor muscle tone, balance and coordination.
Can a baby survive with Dandy Walker syndrome?
Some people with Dandy-Walker complex may have physical disabilities or intellectual disabilities . In most cases, infants who have isolated Dandy-Walker variant are more likely to have normal outcomes in the newborn period.
Can Dandy-Walker Variant be misdiagnosed?
A incorrect diagnosis of the variant form can be made at gestational ages of less than 18 weeks because the cerebellar vermis may not yet be completely developed.
What is Dandy Walker Variant symptoms?
The symptoms of Dandy Walker syndrome typically include developmental delay, low tone (hypotonia) or later high tone (spasticity), poor coordination and balance (ataxia), and sometimes enlarged head circumference and increased pressure within the skull due to hydrocephalus.
What causes hydrocephalus in Dandy Walker?
The Dandy-Walker syndrome is hydrocephalus associated with a posterior fossa cyst and abnormal development of the cerebellum, a portion of the brain located near the base of the skull and important to voluntary muscle movement, balance and posture.
Can you live a normal life with Dandy Walker?
What is a dandy walker baby?
What is Dandy-Walker Syndrome? Dandy-Walker Syndrome (DWS) is a congenital (happening before birth) condition where the cerebellum does not develop normally. The cerebellum is an area at the back of the brain that controls movement and balance. With DWS, parts of the cerebellum may never develop or may be very small.
What is Daniel Walker syndrome?
Dandy-Walker Syndrome is a congenital brain malformation involving the cerebellum (an area at the back of the brain that controls movement) and the fluid-filled spaces around it.
What is Danny Walker disease?
Can a baby live without a cerebellum?
The cerebellum controls smooth movement, and when it does not develop, the rest of the brain must compensate, which it cannot do completely. The condition is not fatal on its own, but people born without a cerebellum experience severe developmental delays, language deficits, and neurological abnormalities.
What are the symptoms of Dandy-Walker malformation?
Children with Dandy-Walker malformation often have delayed development, particularly a delay in motor skills such as crawling, walking, and coordinating movements. People with Dandy-Walker malformation may experience muscle stiffness and partial paralysis of the lower limbs (spastic paraplegia), and they may also have seizures.
What is Dandy-Walker syndrome?
Dandy-Walker syndrome, also known as the Dandy-Walker malformation, is a rare, congenital hydrocephalus (a buildup of fluid in the brain) that affects the cerebellum portion of the brain. The condition, which occurs in one in every 25,000 to 35,000 live births each year, causes different parts of the cerebellum to develop abnormally.
How does Dandy-Walker malformation affect brain development?
Dandy-Walker malformation affects brain development, primarily development of the cerebellum, which is the part of the brain that coordinates movement. In individuals with this condition, various parts of the cerebellum develop abnormally, resulting in malformations that can be observed with medical imaging.
Can Dandy-Walker complex affect other body parts?
In some cases, Dandy-Walker complex can be a sign of a separate underlying genetic syndrome. Therefore, some people with Dandy-Walker complex have other health problems or differences from birth that can affect other parts of the brain as well as the heart, face, limbs, fingers, and toes.